{"created":"2023-05-15T09:02:53.878188+00:00","id":3782,"links":{},"metadata":{"_buckets":{"deposit":"aa5ce3f2-18c7-4eb3-a079-1a38225a5af6"},"_deposit":{"created_by":3,"id":"3782","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"3782"},"status":"published"},"_oai":{"id":"oai:hirosaki.repo.nii.ac.jp:00003782","sets":["557:561:654"]},"author_link":["13849","11090","11094","13841","13847","13856","13850","13857","13855","14468","13846","13840","13858","13848","11086","13843","11436","13844","13853","13845","14447","11439","13851"],"item_3_biblio_info_8":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2013-04-02","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"Supplement","bibliographicPageEnd":"S89","bibliographicPageStart":"S86","bibliographicVolumeNumber":"64","bibliographic_titles":[{"bibliographic_title":"弘前医学"}]}]},"item_3_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"X-linked recessive anhidrotic ectodermal dysplasia with immunodeficiency( XL-EDA-ID) is a congenital developmental and immunologic disorder, which often causes osteopetrosis. These individuals are susceptible to infection with various microorganisms, and most patients die of infection before reaching maturity. Hematopoietic stem cell transplantation (HSCT) is considered the only cure for this disorder. When HSCT is performed in patients with osteopetrosis, on the other hand, transient hypercalcemia often occurs in these patients. We report a XL-EDA-ID patient with osteopetrosis who experienced hypercalcemia and resolution of bone changes after cord blood transplantation.","subitem_description_type":"Abstract"}]},"item_3_description_7":{"attribute_name":"引用","attribute_value_mlt":[{"subitem_description":"弘前医学. 64(Suppl.), 2013, p.S86-S89","subitem_description_type":"Other"}]},"item_3_full_name_2":{"attribute_name":"著者(ヨミ)","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifier":"13847","nameIdentifierScheme":"WEKO"}],"names":[{"name":"ササキ, シンヤ"}]},{"nameIdentifiers":[{"nameIdentifier":"13848","nameIdentifierScheme":"WEKO"}],"names":[{"name":"カミオ, タクヤ"}]},{"nameIdentifiers":[{"nameIdentifier":"13849","nameIdentifierScheme":"WEKO"}],"names":[{"name":"クドウ, コウ"}]},{"nameIdentifiers":[{"nameIdentifier":"13850","nameIdentifierScheme":"WEKO"}],"names":[{"name":"サトウ, トモヒコ"}]},{"nameIdentifiers":[{"nameIdentifier":"13851","nameIdentifierScheme":"WEKO"}],"names":[{"name":"トオノ, チカコ"}]},{"nameIdentifiers":[{"nameIdentifier":"11439","nameIdentifierScheme":"WEKO"}],"names":[{"name":"タカハシ, ヨシヒロ"}]},{"nameIdentifiers":[{"nameIdentifier":"13853","nameIdentifierScheme":"WEKO"}],"names":[{"name":"テルイ, キミノリ"}]},{"nameIdentifiers":[{"nameIdentifier":"11090","nameIdentifierScheme":"WEKO"}],"names":[{"name":"イトウ, エツロウ"}]}]},"item_3_full_name_3":{"attribute_name":"著者別名","attribute_value_mlt":[{"nameIdentifiers":[{"nameIdentifier":"13855","nameIdentifierScheme":"WEKO"}],"names":[{"name":"佐々木, 伸也"}]},{"nameIdentifiers":[{"nameIdentifier":"13856","nameIdentifierScheme":"WEKO"}],"names":[{"name":"神尾, 卓哉"}]},{"nameIdentifiers":[{"nameIdentifier":"14447","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"249","nameIdentifierScheme":"研究者総覧","nameIdentifierURI":"http://hue2.jm.hirosaki-u.ac.jp/html/249_ja.html"}],"names":[{"name":"工藤, 耕"}]},{"nameIdentifiers":[{"nameIdentifier":"13857","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"100000294","nameIdentifierScheme":"研究者総覧","nameIdentifierURI":"http://hue2.jm.hirosaki-u.ac.jp/html/100000294_ja.html"}],"names":[{"name":"佐藤, 知彦"}]},{"nameIdentifiers":[{"nameIdentifier":"11436","nameIdentifierScheme":"WEKO"}],"names":[{"name":"高橋, 良博"}]},{"nameIdentifiers":[{"nameIdentifier":"13858","nameIdentifierScheme":"WEKO"},{"nameIdentifier":"450","nameIdentifierScheme":"研究者総覧","nameIdentifierURI":"http://hue2.jm.hirosaki-u.ac.jp/html/450_ja.html"}],"names":[{"name":"照井, 君典"}]},{"nameIdentifiers":[{"nameIdentifier":"11086","nameIdentifierScheme":"WEKO"}],"names":[{"name":"伊藤, 悦朗"}]}]},"item_3_publisher_35":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"弘前大学大学院医学研究科・弘前医学会"}]},"item_3_radio_42":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"subitem_radio_item":"Article"}]},"item_3_source_id_11":{"attribute_name":"書誌レコードID","attribute_value_mlt":[{"subitem_source_identifier":"AN00211444","subitem_source_identifier_type":"NCID"}]},"item_3_source_id_9":{"attribute_name":"ISSN","attribute_value_mlt":[{"subitem_source_identifier":"0439-1721","subitem_source_identifier_type":"ISSN"}]},"item_3_subject_19":{"attribute_name":"日本十進分類法","attribute_value_mlt":[{"subitem_subject":"490","subitem_subject_scheme":"NDC"}]},"item_3_subject_23":{"attribute_name":"NIIサブジェクト","attribute_value_mlt":[{"subitem_subject":"医学","subitem_subject_scheme":"Other"}]},"item_3_text_4":{"attribute_name":"著者所属","attribute_value_mlt":[{"subitem_text_value":"Department of Pediatrics, Hirosaki University Graduate School of Medicine"}]},"item_3_version_type_18":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Sasaki, Shinya"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Kamio, Takuya"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"Kudo, Ko"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"Sato, Tomohiko"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"Tono, Chikako"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Takahashi, Yoshihiro"}],"nameIdentifiers":[{}]},{"creatorNames":[{"creatorName":"Terui, Kiminori"}],"nameIdentifiers":[{},{}]},{"creatorNames":[{"creatorName":"Ito, Etsuro"}],"nameIdentifiers":[{}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2018-03-13"}],"displaytype":"detail","filename":"HirosakiMedJ_64_S86.pdf","filesize":[{"value":"298.7 kB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"HirosakiMedJ_64_S86.pdf","url":"https://hirosaki.repo.nii.ac.jp/record/3782/files/HirosakiMedJ_64_S86.pdf"},"version_id":"f1490100-f449-4252-9314-caab4d7ea9d3"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"NF-kappa B","subitem_subject_scheme":"Other"},{"subitem_subject":"NEMO","subitem_subject_scheme":"Other"},{"subitem_subject":"transplantation","subitem_subject_scheme":"Other"},{"subitem_subject":"osteopetrosis","subitem_subject_scheme":"Other"},{"subitem_subject":"hypercalcemia","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_title":"Hypercalcemia FOllowing Umbilical Cord Blood Transplantation to Correct Osteopetrosis Associated with the Nemo Mutation","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"Hypercalcemia FOllowing Umbilical Cord Blood Transplantation to Correct Osteopetrosis Associated with the Nemo Mutation"}]},"item_type_id":"3","owner":"3","path":["654"],"pubdate":{"attribute_name":"公開日","attribute_value":"2013-04-30"},"publish_date":"2013-04-30","publish_status":"0","recid":"3782","relation_version_is_last":true,"title":["Hypercalcemia FOllowing Umbilical Cord Blood Transplantation to Correct Osteopetrosis Associated with the Nemo Mutation"],"weko_creator_id":"3","weko_shared_id":3},"updated":"2023-05-15T09:41:58.560378+00:00"}